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Rare (Under 1 in 2000)

Facts
Comparison
ICD-10 Chapter Number
III 1
ICD-10 Code Range
D50-D89 1
Rare (Under 1 in 2000)
Filter Results39 entries

Adenosine deaminase 2 deficiency

Rare (Under 1 in 2000)

AL amyloidosis

Rare (Under 1 in 2000)

Antiphospholipid Syndrome

Rare (Under 1 in 2000)

Atypical hemolytic uremic syndrome

Rare (Under 1 in 2000)

Castleman disease

Rare (Under 1 in 2000)

Chronic Granulomatous Disease

Rare (Under 1 in 2000)

Congenital amegakaryocytic thrombocytopenia

Rare (Under 1 in 2000)

Congenital dyserythropoietic anemia

Rare (Under 1 in 2000)

Cyclic neutropenia

Rare (Under 1 in 2000)

Diamond-Blackfan anemia

Rare (Under 1 in 2000)

DiGeorge Syndrome

Rare (Under 1 in 2000)

Epstein syndrome

Rare (Under 1 in 2000)

Factor XII deficiency

Rare (Under 1 in 2000)

Fanconi anemia

Rare (Under 1 in 2000)

Granulomatosis with Polyangiitis

Rare (Under 1 in 2000)

Griscelli syndrome type 2

Rare (Under 1 in 2000)

Hereditary elliptocytosis

Rare (Under 1 in 2000)

Hereditary Spherocytosis

Rare (Under 1 in 2000)

Hoyeraal-Hreidarsson syndrome

Rare (Under 1 in 2000)

Hughes-Stovin Syndrome

Rare (Under 1 in 2000)

Hypereosinophilic syndrome

Rare (Under 1 in 2000)

Immunodeficiency-centromeric instability-facial anomalies syndrome

Rare (Under 1 in 2000)

LIG4 syndrome

Rare (Under 1 in 2000)

Muckle-Wells syndrome

Rare (Under 1 in 2000)

Paroxysmal nocturnal hemoglobinuria

Rare (Under 1 in 2000)

Purine nucleoside phosphorylase deficiency

Rare (Under 1 in 2000)

Quebec platelet disorder

Rare (Under 1 in 2000)

Scleroderma

Rare (Under 1 in 2000)

Scott syndrome

Rare (Under 1 in 2000)

Severe Combined Immunodeficiency

Rare (Under 1 in 2000)

Severe congenital neutropenia

Rare (Under 1 in 2000)

Systemic Lupus Erythematosus

Rare (Under 1 in 2000)

Thiamine responsive megaloblastic anemia syndrome

Rare (Under 1 in 2000)

Thrombotic thrombocytopenic purpura

Rare (Under 1 in 2000)

Von Willebrand Disease

Rare (Under 1 in 2000)

WHIM syndrome

Rare (Under 1 in 2000)

Wiskott-Aldrich Syndrome

Rare (Under 1 in 2000)

X-linked agammaglobulinemia

Rare (Under 1 in 2000)

X-linked lymphoproliferative disease

Rare (Under 1 in 2000)
Sources
1. ICD-10 (Wikipedia)
  • ICD-10 chapter table, Chapter III, chapter number
    III | D50-D89 | "Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism"
  • ICD-10 chapter table, Chapter III, code range
    III | D50-D89 | "Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism"
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