Gastrocutaneous syndrome is a rare autosomal dominant condition combining multiple lentigines and cafe-au-lait spots with peptic ulcer or hiatal hernia, hypertelorism, and myopia. It is classified among the genodermatoses, inherited skin conditions with effects reaching beyond the skin itself.
Facts
Classification
ICD-10 ChapterXII: Diseases of the Skin and Subcutaneous Tissue 1 Communicable or Non-communicable Causative Agent
Causative Agent (category) Prevalence Band Sources
1. Wikipedia: ICD-10
WikipediaList of chapters, Chapter XIIQuote, List of chapters, Chapter XII
Diseases of the skin and subcutaneous tissue
2. Gastrocutaneous syndrome (Wikipedia)
- lead: a rare autosomal dominant cutaneous condition
lead sentence 1
Gastrocutaneous syndrome is a rare autosomal dominant cutaneous condition characterized by multiple lentigines.
View the Source3. Orphadata (Orphanet): Orphadata: Epidemiology of rare diseases (en_product9_prev)
Orphadata (Orphanet)ORPHA:2069Quote, ORPHA:2069
Point prevalence Class only <1 / 1 000 000
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