Double outlet right ventricle

Double outlet right ventricle, usually abbreviated DORV, is a form of congenital heart disease in which both of the body's great arteries, the aorta and the pulmonary artery, connect wholly or partly to the heart's right ventricle rather than following the normal pattern in which the aorta arises from the left ventricle and the pulmonary artery from the right. In rarer described cases the analogous defect occurs on the left side of the heart instead. Because both great vessels arise from the same chamber, DORV disrupts the normal separation between oxygen-rich blood destined for the body and oxygen-poor blood destined for the lungs, and it is typically diagnosed in infancy alongside other structural heart findings that determine how blood actually flows and what symptoms result. Chromosomal abnormalities have been reported in about 40 percent of documented cases in the medical literature, pointing to a substantial genetic component in many instances even though a specific cause is not identified in every case. The defect is recognized in standard diagnostic classifications, including ICD-10 code Q20.1 and OMIM entry 217095, reflecting its status as a well-characterized, named category of congenital heart malformation.