Chronic thromboembolic pulmonary hypertension

Chronic thromboembolic pulmonary hypertension, known by the abbreviation CTEPH, is characterized by the persistence of thromboemboli, blood clots that have turned into organized tissue, which obstruct the pulmonary arteries. The consequence is a rise in pulmonary vascular resistance, which results in pulmonary hypertension and progressive failure of the right side of the heart. Reference systems classify it under ICD-10-CM code I27.24, OMIM entry 612862 and Orphanet entry 70591, which places it among the diseases of the circulatory system. This entry records the condition as the ontology defines it and gives no clinical guidance.